• Vladimir Pfeifer Očesna klinika Klinični center Zaloška 29 1525 Ljubljana
  • Kristina Mikek Očesna klinika Klinični center Zaloška 29 1525 Ljubljana
Keywords: ectopia lentis, surgical technique, Cionni endocapsular tension ring, dry irrigation aspiration of lens material, IOL implantation


Background. Ectopia lentis continues to be a therapeutic challenge for ophthalmologists. It can occur as an isolated condition, after ocular trauma, in association with other ocular disorders, as part of a systemic mesodermal disease or a complication of general metabolic disorders. Minimal subluxation of the lens may cause no visual symptoms, but in more advanced cases serious optical disturbances arise. The most important is amblyopia. Surgical treatment options include iris manipulation, lens discission, aspiration, intracapsular or extracapsular extraction, and pars plana lensectomy. The choice of surgical technique remains controversial, in part because of the historically poor visual results and high rate of perioperative complications, including vitreous loss and retinal detachment.

Methods. We describe a surgical technique based on the use of the Cionni endocapsular tension ring, dry irrigation aspiration of lens material, centration of the capsular bag and foldable intraocular lens implantation into the bag. With mentioned surgical technique 8 patients were operated; 4 boys and 4 girls, together 11 eyes.

Results. The final BCVA after follow up period improved in 9 eyes and it remained the same as before operation in one eye. Statistical comparison of preoperative and postoperative visual acuities showed significant improvement. On the other hand there was no correlation between preoperative and postoperative visual acuity.

Conclusions. This surgical procedure is an alternative approach in solving this challenging cases of ectopia lentis with good postoperative visual rehabilitation.


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How to Cite
Pfeifer V, Mikek K. ECTOPIC LENS EXTRACTION IN CHILDREN. ZdravVestn [Internet]. 1 [cited 26Mar.2019];71. Available from:
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